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Iranian Journal of Neonatology، جلد ۱۲، شماره ۳، صفحات ۱۱۰-۱۱۵
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| عنوان فارسی |
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| چکیده فارسی مقاله |
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| کلیدواژه‌های فارسی مقاله |
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| عنوان انگلیسی |
Urinary Type Hydrometrocolpos and Polydactyly in Two Newborns: Case Report |
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| چکیده انگلیسی مقاله |
Background: Abdominal masses secondary to urinary retention are rare among female neonates and approaching this pathologic condition, inevitably, poses a diagnostic challenge. Hydrometrocolpos is one example of this disease category which is responsible for only 15% of such cases whose association with polydactyly appears to be even less common. The present study aimed to report the accounts of two neonates with cystic abdominal masses diagnosed as urinary type hydrometrocolpos secondary to urogenital sinus anomaly. Autosomal recessive disorders are characterized by vaginal atresia with hydrometrocolpos, polydactyly, congenital heart defects, and non-immune mediated hydrops fetalis. The triad of hydrometrocolpos, polydactyly, and cardiac anomaly in the two patients presented herein is strongly suggestive of a case of McKusick-Kaufman syndrome. Case report: This study reported two neonates with abdominal mass, polydactyly, and genitourinary tract malformation, with no family history. Relief of urinary obstruction by exploratory laparotomy, aspiration of fluid, and vaginal reconstruction gradually reversed the hydronephrosis and renal failure. Conclusion: It can be concluded thatin hydrometrocolpos causing urinary obstruction, decompression of hydrometrocolpos can save the kidneys. |
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| کلیدواژه‌های انگلیسی مقاله |
hydrometrocolpos, McKusick–Kaufman syndrome, polydactyly |
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| نویسندگان مقاله |
| Ziba Mosayebi
Family Health Institute, Maternal-Fetal and Neonatal Research Center, Tehran University of Medical Sciences, Tehran, Iran
| Tahereh Esmaeilnia Shirvani
Family Health Institute, Maternal-Fetal and Neonatal Research Center, Tehran University of Medical Sciences, Tehran, Iran
| Vafa Ghorban Sabagh
Breastfeeding Research Center, Tehran University of Medical Sciences, Tehran, Iran
| Maryam Ghavami-Adel
Department of Pediatric Surgery, Tehran University of Medical Sciences, Tehran, Iran
| Bahareh Fasihpour
Breastfeeding Research Center, Tehran University of Medical Sciences, Tehran, Iran
| Hosein Dalili
Breastfeeding Research Center, Tehran University of Medical Sciences, Tehran, Iran
| Ali Fathi
Breastfeeding Research Center, Tehran University of Medical Sciences, Tehran, Iran
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| نشانی اینترنتی |
https://ijn.mums.ac.ir/article_18477.html |
| فایل مقاله |
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| کد مقاله (doi) |
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| زبان مقاله منتشر شده |
en |
| موضوعات مقاله منتشر شده |
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| نوع مقاله منتشر شده |
گزارش موارد نادر |
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